TY - CHAP M1 - Book, Section TI - PRIMARY BULLOUS DERMATOSES A1 - Kane, Kay Shou-Mei A1 - Nambudiri, Vinod E. A1 - Stratigos, Alexander J. PY - 2016 T2 - Color Atlas & Synopsis of Pediatric Dermatology, 3e AB - Epidermolysis bullosa (EB) defines a group of rare inherited mechanobullous skin disorders that are characterized by skin fragility and bullae formation. There are three major categorizations of the disease: epidermolysis bullosa simplex (EBS), junctional epidermolysis bullosa (JEB), and dystrophic epidermolysis bullosa (DEB) with over 20 different phenotypes representing mutations in the genes of at least 18 structural proteins of the skin (in the epidermis, dermal–epidermal junction, or upper papillary dermis). SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - dermatology.mhmedical.com/content.aspx?aid=1133126139 ER -