TY - CHAP M1 - Book, Section TI - Paraneoplastic Pemphigus A1 - Anhalt, Grant J. A1 - Mimouni, Daniel A2 - Kang, Sewon A2 - Amagai, Masayuki A2 - Bruckner, Anna L. A2 - Enk, Alexander H. A2 - Margolis, David J. A2 - McMichael, Amy J. A2 - Orringer, Jeffrey S. PY - 2019 T2 - Fitzpatrick's Dermatology, 9e AB - AT-A-GLANCERare complication of malignancy, most commonly non-Hodgkin lymphoma, chronic lymphocytic leukemia, or Castleman disease.Painful, erosive stomatitis and polymorphous cutaneous lesions that may be blistering and erosive (resembling erythema multiforme), morbilliform, or lichenoid.Serum autoantibodies directed against plakin proteins that are detected by indirect immunofluorescence against rodent bladder epithelium.High mortality rate, with death from sepsis, complications of treatment, or bronchiolitis obliterans.No consistently effective therapy, but some success with the combined use of rituximab, systemic corticosteroids, and other immunosuppressive agents. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - dermatology.mhmedical.com/content.aspx?aid=1161331481 ER -