RT Book, Section A1 Anhalt, Grant J. A1 Mimouni, Daniel A2 Kang, Sewon A2 Amagai, Masayuki A2 Bruckner, Anna L. A2 Enk, Alexander H. A2 Margolis, David J. A2 McMichael, Amy J. A2 Orringer, Jeffrey S. SR Print(0) ID 1161331481 T1 Paraneoplastic Pemphigus T2 Fitzpatrick's Dermatology, 9e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9780071837798 LK dermatology.mhmedical.com/content.aspx?aid=1161331481 RD 2024/11/02 AB AT-A-GLANCERare complication of malignancy, most commonly non-Hodgkin lymphoma, chronic lymphocytic leukemia, or Castleman disease.Painful, erosive stomatitis and polymorphous cutaneous lesions that may be blistering and erosive (resembling erythema multiforme), morbilliform, or lichenoid.Serum autoantibodies directed against plakin proteins that are detected by indirect immunofluorescence against rodent bladder epithelium.High mortality rate, with death from sepsis, complications of treatment, or bronchiolitis obliterans.No consistently effective therapy, but some success with the combined use of rituximab, systemic corticosteroids, and other immunosuppressive agents.