RT Book, Section A1 Zouboulis, Christos C. A2 Kang, Sewon A2 Amagai, Masayuki A2 Bruckner, Anna L. A2 Enk, Alexander H. A2 Margolis, David J. A2 McMichael, Amy J. A2 Orringer, Jeffrey S. SR Print(0) ID 1161350001 T1 Adamantiades–Behçet Disease T2 Fitzpatrick's Dermatology, 9e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9780071837798 LK dermatology.mhmedical.com/content.aspx?aid=1161350001 RD 2024/04/24 AB AT-A-GLANCERare disease with worldwide distribution but strongly varying prevalence; certain ethnic groups are mainly affected.A genetically determined disorder with a probable environmental triggering factor.Multisystem occurrence, with oral aphthous ulcers, genital ulcers, papulopustules, erythema nodosum–like lesions, uveitis, and arthropathy as the most common signs.Inflammatory disease representing a neutrophilic vascular reaction or vasculitis.Chronic, relapsing, and progressive course with a potentially poor prognosis (especially in males with systemic presenting signs; mortality, 0%-6%).